Alpha-Synuclein (α-Syn)
Category: biomarker
A presynaptic protein that misfolds and forms Lewy body aggregates in Parkinson's disease. A central biomarker and therapeutic target.
Mechanism Detail
α-Synuclein normally regulates synaptic vesicle trafficking and neurotransmitter release. In Parkinson's, it misfolds into β-sheet-rich oligomers and fibrils that propagate cell-to-cell in a prion-like manner. Aggregates impair mitochondrial function, lysosomal degradation, and proteasomal clearance. SNCA gene duplication/triplication and point mutations (A53T, A30P) cause familial PD.
Clinical Status
Anti-α-synuclein antibodies (prasinezumab) in Phase II trials showed mixed results. α-Synuclein seed amplification assay (SAA) is emerging as a diagnostic biomarker. ASO approaches targeting SNCA mRNA are in development.
Relevant Diseases
- Parkinson's Disease
Relevant Therapies
- Gene Therapy
- Peptides
Related Terms
- Lewy bodies
- LRRK2
- Prion-like spreading
- Dopaminergic neurons